<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0378-6420</journal-id>
<journal-title><![CDATA[Revista Venezolana de Cirugía]]></journal-title>
<abbrev-journal-title><![CDATA[RevVenezCir]]></abbrev-journal-title>
<issn>0378-6420</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Venezolana de Cirugía]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0378-64202024000100053</article-id>
<article-id pub-id-type="doi">10.48104/rvc.2024.77.1.14</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[INTUSUSCEPCIÓN INTESTINAL MÁS GRANDE REPORTADA EN PACIENTE CON SÍNDROME DE PEUTZ-JEGHERS. INFORME DE CASO]]></article-title>
<article-title xml:lang="en"><![CDATA[Larger intestinal intussusception reported in a patient with Peutz-Jeghers syndrome. Case report]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Vassallo P]]></surname>
<given-names><![CDATA[Miguel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Oliveros C]]></surname>
<given-names><![CDATA[Alexis]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Bravo]]></surname>
<given-names><![CDATA[Sailú]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Acero]]></surname>
<given-names><![CDATA[Carlos]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Durán]]></surname>
<given-names><![CDATA[Bárbara]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Vieira]]></surname>
<given-names><![CDATA[Daniela]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Universitario de Caracas  ]]></institution>
<addr-line><![CDATA[Caracas ]]></addr-line>
<country>Venezuela</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital Universitario de Caracas  ]]></institution>
<addr-line><![CDATA[Caracas ]]></addr-line>
<country>Venezuela</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Hospital Universitario de Caracas UCV  ]]></institution>
<addr-line><![CDATA[Caracas ]]></addr-line>
<country>Veneuela</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Hospital Universitario de Caracas  ]]></institution>
<addr-line><![CDATA[Caracas ]]></addr-line>
<country>Venezuela</country>
</aff>
<aff id="Af5">
<institution><![CDATA[,Universidad Central de Venezuela  ]]></institution>
<addr-line><![CDATA[Caracas ]]></addr-line>
<country>Venezuela</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>06</month>
<year>2024</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>06</month>
<year>2024</year>
</pub-date>
<volume>77</volume>
<numero>1</numero>
<fpage>53</fpage>
<lpage>56</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://hml-ve.scielo.org/scielo.php?script=sci_arttext&amp;pid=S0378-64202024000100053&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://hml-ve.scielo.org/scielo.php?script=sci_abstract&amp;pid=S0378-64202024000100053&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://hml-ve.scielo.org/scielo.php?script=sci_pdf&amp;pid=S0378-64202024000100053&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción:  La intususcepción intestinal se considera una causa rara de obstrucción intestinal en adultos, sus efectos son graves y a menudo requieren intervención quirúrgica, su diagnóstico es un reto dada sus manifestaciones clínicas inespecíficas. El síndrome de Peutz-Jeghers es una enfermedad genética poco frecuente, caracterizada por la presencia de pólipos hamartomatosos intestinales y pigmentaciones mucocutáneas. Durante su crecimiento dichos pólipos pueden llegar a complicarse y causar intususcepción, obstrucción y hemorragias intestinales.  Caso clínico:  femenina de 18 años con diagnóstico de SPJ, quien refiere inicio de enfermedad actual 13 días previos a su ingreso, caracterizado por dolor tipo cólico de moderada intensidad en epigastrio, evacuaciones líquidas, en número de 5 al día, sin moco ni sangre, náuseas y vómitos de contenido alimentario en múltiples oportunidades. Se realizó US abdominal evidenciando imagen redondeada en epigastrio hipoecoica de 78.4mm x 49.3mm. Fue llevada a mesa operatoria bajo el diagnóstico de Abdomen agudo Obstructivo secundario a: Intususcepción. Los hallazgos quirúrgicos reportaron un Intusuceptum yeyunal de 60cm con cambios isquémicos irreversibles, por lo que se decide realizar resección y anastomosis, evolucionando de forma satisfactoria  Conclusión:  Evaluando la literatura disponible la intususcepción intestinal más larga hasta ahora reportada es de 50 cm por lo tanto nuestro trabajo pretende aportar nueva información y memoria académica sobre esta entidad clínica.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Introduction:  Intestinal intussusception is considered a rare cause of intestinal obstruction in adults, its effects are serious and often require surgical intervention, its diagnosis is a challenge given its non-specific clinical manifestations. Peutz-Jeghers syndrome is a rare genetic disease, characterized by the presence of intestinal hamartomatous polyps and mucocutaneous pigmentations. During their growth, these polyps can become complicated and cause intussusception, obstruction and intestinal bleeding.  Clinical case:  of an 18-year-old female with a diagnosis of PJS, who reported the onset of current illness 13 days prior to her admission, characterized by colicky pain of moderate intensity in the epigastrium, liquid stools, 5 per day, without mucus. nor blood, nausea and vomiting of food content on multiple occasions. An abdominal US was performed showing a rounded image in the hypoechoic epigastrium measuring 78.4mm x 49.3mm. She was taken to the operating table under the diagnosis of Acute Obstructive Abdomen secondary to: Intussusception. The surgical findings reported a jejunal intussusception of 60cm with irreversible ischemic changes, so it was decided to perform resection and anastomosis, progressing satisfactorily  Conclusion:  Evaluating the available literature, the longest intestinal intussusception reported so far is 50cm, therefore our work aims to provide new information and academic memory about this clinical entity.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Caso clínico]]></kwd>
<kwd lng="es"><![CDATA[Síndrome de Peutz-Jeghers]]></kwd>
<kwd lng="es"><![CDATA[Intususcepción]]></kwd>
<kwd lng="es"><![CDATA[Obstrucción Intestinal]]></kwd>
<kwd lng="es"><![CDATA[Poliposis Intestinal]]></kwd>
<kwd lng="en"><![CDATA[Clinical case]]></kwd>
<kwd lng="en"><![CDATA[Peutz-Jeghers Syndrome]]></kwd>
<kwd lng="en"><![CDATA[Intussusception]]></kwd>
<kwd lng="en"><![CDATA[Intestinal Obstruction]]></kwd>
<kwd lng="en"><![CDATA[Intestinal Polyposis]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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